Complement‐activating ability of leucocytes from patients with‘qc complement factor I deficiency

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A family with complement factor I deficiency.

A family with inherited factor I deficiency is described. The proband was a 19-year-old Caucasian female with one episode of meningococcal meningitis and one episode of suspected septicaemia of unknown cause. Two obligate and two probable heterozygotes with factor I levels below the lower limit of the reference range were identified. None of these exhibited increased susceptibility to infectiou...

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ژورنال

عنوان ژورنال: Immunology

سال: 1997

ISSN: 0019-2805,1365-2567

DOI: 10.1046/j.1365-2567.1997.00273.x